Pulmonary Surfactant Metabolism in Infants Lacking Surfactant Protein B
نویسندگان
چکیده
منابع مشابه
Pulmonary surfactant metabolism in infants lacking surfactant protein B.
Infants with inherited deficiency of pulmonary surfactant protein (SP) B develop respiratory failure at birth and die without lung transplantation. We examined aspects of surfactant metabolism in lung tissue and lavage fluid acquired at transplantation or postmortem from ten infants born at term with inherited deficiency of SP-B; comparison groups were infants with other forms of chronic lung d...
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ژورنال
عنوان ژورنال: American Journal of Respiratory Cell and Molecular Biology
سال: 2000
ISSN: 1044-1549,1535-4989
DOI: 10.1165/ajrcmb.22.3.3645